Pancreatic Cyst in von Hippel–Lindau Disease: A Case Report
SHARZIA ASMA–UL HOSNA1, BISHWAJIT BHOWMIK2, MAHBOOBA SHIRIN3, MAHESH CHAUDHARY4, SAYEEDA SHOWKAT5, SHAILA JABEEN6
Abstract
Von Hippel–Lindau (VHL) disease is a rare autosomal dominant, inherited familial syndrome with an incidence of 2–3 cases per 100,000 populations. Approximately 65–75% of patients with VHL has multi-visceral tumors with some form of pancreatic lesions (cystic and solid tumours).